Alagille Syndrome
Risk • Also known as syndromic bile duct paucity • Affects cardiac, musculoskeletal, ocular, facial, and neurodevelopmental systems • Most common inherited disorder that causes chronic liver disease in children…
Adrenal Insufficiency, Acute or Secondary
Risk • Risk of adrenal insufficiency: 1/1000 to 1/10,000 (if steroids used in prior y). • With steroids >20 mg/d (cortisol equivalent), >7 to 14 d within 1 y (large…
Addison Disease
Risk • Prevalence 1:100,000 persons • M:F ratio: 1:1.8 Perioperative Risks • CV instability, labile BP, hypotension, shock • Hypovolemia, hyperkalemia, cardiac dysrhythmia • Limited response to vasopressors Perioperative Risks…
Acute Respiratory Distress Syndrome
Risk • Recent data estimates the incidence at 190,000 cases per year in USA. True incidence is unknown due to difficulty in defining the disease and making the diagnosis. •…
Acute Intermittent Porphyria
Risk • Prevalence: <200,000 cases of porphyria in USA, AIP: 5 to 10 in 100,000 worldwide. • Highest in Northern Europeans. • More commonly manifests in females, typically third to…
Acromegaly
Risk • People within USA: • Prevalence is 40 cases/million; incidence is 3 to 8 new cases/million/y. • Occurs with equal frequency in men and women and most frequently diagnosed…
Acquired Immunodeficiency Syndrome
Risk • USA incidence of HIV: 50,000 per year • USA prevalence of HIV: 1.2 million • Sub-Saharan Africa prevalence: 25.8 million in 2014 • USA prevalence of AIDS (HIV…
Acidosis, Renal Tubular
Risk • Incidence in USA: Unknown • Present in a variety of disease states, from mild to severe systemic illness Perioperative Risks • Hemodynamic instability (related to arteriolar vasodilation, acidosis,…
Acidosis, Lactic/Metabolic
Risk • Incidence in USA: Unknown • Present in a variety of disease states, from mild to severe systemic illness Perioperative Risks • Hemodynamic instability (due to arteriolar vasodilation and…
Achondroplasia, Dwarfism
Risk • 1 per 15,000 to 40,000 births worldwide • Females ≥ males • No race predilection • Most common type of dwarfism Perioperative Risks • Cervical spine instability •…
