Porphyrias
Abstract Porphyria is a rare inherited metabolic disorder that results from mutations in the genes coding for the enzymes involved in heme biosynthesis. Deficiency of these enzymes leads to a…
Perioperative Management of Patients With Muscular Dystrophy
Abstract Muscular dystrophies are a genetically and clinically diverse group of hereditary disorders of the structure of skeletal and cardiac muscle. Abnormal striated muscle and myocardial damage with associated cardiomyopathy…
Patients With Seizure Disorder
Abstract Epilepsy is a neurologic disease with a yearly incidence of 0.5% to 2.3%, with up to 40% of patients developing intractable disease. Seizures can manifest as either partial seizures…
Patients With a Cardiovascular Implantable Electronic Device Undergoing Surgery
Abstract Patients with a cardiovascular implantable electronic device (CIED) routinely undergo surgery, and the perioperative management of these patients is complex and challenging. The presence of one of these devices…
Mechanical Assist Devices
Abstract Mechanical circulatory assist devices are used to support the failing heart. They range in complexity from the intraaortic balloon pump (IABP) to highly sophisticated second- and third-generation ventricular assist…
Myasthenic Disorders
Abstract Myasthenic syndromes encompass a group of neuromuscular disorders that are characterized by weakness and fatigability but also vary in clinical presentations and diagnostic and therapeutic approaches. Myasthenic disorders may…
Patient Confidentiality
Abstract Respect for patient privacy is a pillar of the doctor-patient relationship, and laws codify the duties of doctors to maintain confidentiality with regard to patient interactions. On the other…
Hyperthyroidism: Thyroid Storm
Abstract Hyperthyroidism is a common clinical problem associated with thyroid gland hyperactivity. Complications include thyrotoxicosis and thyroid storm. Radioiodine uptake can help distinguish the disorders associated with thyrotoxicosis. Multiple stresses…
Hypothyroidism: Myxedema Coma
Abstract Hypothyroidism is a common disease with nonspecific clinical symptoms depending on the severity and the age of onset. Myxedema is a rare and life-threatening subset of hypothyroidism that can…
HIV Infection and AIDS
Keywords HIV, AIDS, HIV and anesthesia, HIV and intensive care Case Synopsis A 34-year-old woman with known human immunodeficiency virus (HIV) infection and a recent diagnosis of acquired immunodeficiency…
